Pathology
Ventricles are inverted.
Aorta is anterior and to the left of the PA. Prefix L is because aorta is left.
Mirror image coronaries.
Associated anomalies
VSD in 80%.
PS in 50%. PS may be valvular or subvalvular and is usually seen in patients with VSD.
Systemic AV valve regurgitation (TR) is seen in 30%.
Dextrocardia in 50%.
WPW syndrome can occur.
Heart blocks can occur. First degree block occurs in 50%. Second degree block can progress to third degree block.
Third degree block occurs in 30%.
Clinical features-
VSD + PS may cause cyanosis (like any VSD + PS).
VSD alone may cause heart failure (like any VSD).
Single S2.
Chest X-ray
Straight left cardiac border is formed by ascending aorta.
Echo
There is no aorto-tricuspid continuity.
PSAX- double circle is seen.
Treatment
